StayCurrentMD · Esophageal Atresia
Video39 min·Published Nov 2018Older

Esophageal Atresia

hosted by Dr. Todd Ponsky · StayCurrentMD
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What the experts said27 expert statements · 8 host summaries
Less than half of esophageal atresia cases are detected antenatally, typically by small stomach and polyhydramnios.
Epidemiological
Echocardiography is performed preoperatively to rule out congenital heart defects and determine aortic arch sidedness (right vs. left).
Clinical
VACTERL workup (renal ultrasound, vertebral X-rays, anorectal exam) can be completed electively after initial repair.
Clinical
Right-sided aortic arch does not necessarily require left thoracotomy; multiple surgeons report successful repairs from the right side despite right arch.
Clinical
Echocardiography may misidentify aortic arch sidedness; one surgeon encountered a double arch after echo reported right arch.
Clinical
Preoperative bronchoscopy can identify double fistulas and predict gap length: fistula at mid-trachea suggests shorter gap, fistula at carina suggests longer gap.
Clinical
For thoracoscopic repair, bronchoscopy helps the surgeon understand fistula location and anticipate gap distance.
Clinical
Standard open approach uses right posterolateral thoracotomy, extrapleural dissection to vertebral bodies, with azygos vein as landmark for fistula location.
Clinical
For uncomplicated EA, tissue interposition between trachea and esophagus is not routinely used because adequate tissue is difficult to find.
Clinical
Chest tube is placed in extrapleural space on water seal (not suction) and removed after postoperative contrast study confirms no leak.
Clinical
Retrospective study of ~100 patients found no difference in complications between Vicryl and silk suture for EA repair.
Clinical
For thoracoscopic repair using knot-pusher technique, PDS must be used for the first stitch to avoid sawing through tissue; Vicryl can be used for intracorporeal ties.
Clinical
Approximately 75% of EA/TEF patients are candidates for thoracoscopic repair; complicated congenital heart disease may preclude thoracoscopic approach due to longer operative time.
Clinical
If the two esophageal ends cannot be approximated thoracoscopically, conversion to open is appropriate—surgeons get one good chance at primary repair.
Opinion
Babies under 2 kg are more difficult for thoracoscopic repair due to limited space for lung retraction and intracorporeal suturing.
Clinical
In US training programs, fellows typically perform 4-8 EA repairs during fellowship, raising questions about adequate thoracoscopic training volume.
Epidemiological
For thoracoscopic repair, ports should be spaced widely and staggered, with patient positioned more prone than lateral since esophagus is posterior mediastinal.
Clinical
High-frequency oscillatory ventilation in the OR keeps the lung collapsed during thoracoscopic repair; disadvantage is the baby shaking, but hypercarbia is avoided.
Clinical
C1 or TF needles (5-0 PDS) are preferred for thoracoscopic EA repair due to appropriate curve and ability to pass through 5-6mm trocars without tip damage.
Clinical
Starting the anastomosis at the lateral (far) corner is most common; some start with a middle back-row stitch tied intracorporeally.
Clinical
The first anastomotic stitch does not need to be tied tight; subsequent stitches are tightened once approximation is confirmed.
Clinical
Exteriorizing the first stitch through the chest wall with a hemostat can help bring the gap closer before placing subsequent sutures.
Clinical
For long-gap atresia (pure EA with gasless abdomen), G-tube placement allows gap assessment; if gap is ≤2 vertebral bodies, primary repair is attempted.
Clinical
Interventional radiology can pass a wire and catheter up the distal esophagus via G-tube to define the gastroesophageal junction and measure gap accurately.
Clinical
Cervical esophagostomy commits the patient to esophageal replacement; most surgeons avoid it and attempt delayed primary anastomosis.
Opinion
For long-gap EA, waiting up to 3 months with G-tube feeds (advancing to bolus feeds to encourage distal esophageal growth) is reasonable before declaring the gap irreparable.
Clinical
Routine bougienage of the proximal pouch does not reliably promote esophageal growth; growth occurs spontaneously over time.
Opinion
Early thoracoscopic series (2008-2010) showed lower stricture rates with thoracoscopic vs. open repair, but more recent data show equivalent stricture rates.
Host summary
Average US attending surgeon performs 1-2 TEF repairs per year, making advanced thoracoscopic technique acquisition challenging.
Host summary
Low-cost training models for EA repair are available and should be used at society meetings (IPEG, APSA) to address low case volume.
Host summary
Marcello reports doing all EA repairs thoracoscopically for over 10 years after performing ~150 open repairs, finding the approach natural and comfortable.
Host summary
Wet clips are a fast and reliable method for dividing the TEF during thoracoscopic repair.
Host summary
Yama's technique: divide only 3/4 of the fistula initially, leaving partial attachment as traction to facilitate anastomosis, then complete division.
Host summary
Passing a transanastomotic feeding tube after back-row sutures provides volume to help guide the needle through the anterior wall.
Host summary
Minimal dissection of the distal esophagus preserves blood supply and reduces trauma, even in long-gap cases.
Host summary