StayCurrentMD · Chronic Pancreatitis, Function Tests, & Pain Management: Pancreatic Disease
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Video51 min·Published Sep 2016Older

Chronic Pancreatitis, Function Tests, & Pain Management: Pancreatic Disease

With Dr. Joe Palermo & Dr. Andrew Trout & Dr. Doctor Goldschneider · hosted by Dr. em gootee · StayCurrentMD
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What the experts said26 expert statements · 13 host summaries
Patients can have acute recurrent pancreatitis without evidence of ductal changes, pancreatic atrophy, or pancreatic function loss.
ClinicalJoe Palermo
In the pediatric cohort, the main risk factors for chronic pancreatitis were genetic, followed by obstructive or anatomic processes.
EpidemiologicalJoe Palermo
In a local cohort of 50 patients (34 ARP, 16 CP), 55% of ARP patients and 68% of CP patients tested positive for mutations in CFTR, PRSS1, CTRC, or SPINK1.
Epidemiological
Chronic pancreatitis patients were diagnosed earlier with the first attack, had more additional attacks, and were more likely to be exocrine insufficient compared to ARP patients.
Epidemiological
CFTR gene was more commonly found in chronic pancreatitis patients compared to acute recurrent patients, and patients were more likely to have two genes affected than one.
Epidemiological
A next-generation sequencing pancreas panel covering 10 genes will launch in October at Cincinnati Children's, offering efficient, low-cost testing with faster turnaround than whole exome sequencing.
Clinical
Heterozygous CFTR (one gene copy) increases the risk for chronic pancreatitis in children.
Clinical
Combination of SPINK1 and CFTR mutations confers an approximately 800-fold relative risk of chronic pancreatitis.
Epidemiological
The CF Foundation has an extensive pipeline of small molecules optimizing CFTR function, which may offer therapeutic options for pancreatitis patients with CFTR mutations.
ClinicalJoe Palermo
Some patients with pancreas divisum do not develop pancreatitis, suggesting a two-hit or multi-hit hypothesis where additional risk factors (e.g., genetic mutations) increase disease propensity.
Opinion
Direct pancreatic function testing means directly obtaining pancreatic function from the pancreas, not relying on stool testing like fecal elastase.
Guideline
The endoscopic pancreatic function test protocol uses secretin (0.2 mcg/kg) or CCK (0.4 mcg/kg) at time zero, then collects duodenal aspirates via ERCP catheter every 5 minutes for three samples.
Clinical
Samples are sent to Women's Children's Hospital lab to measure activities of trypsin, amylase, lipase, and chymotrypsin.
Clinical
Pancreatic function can be abnormal if checked around an acute attack.
Clinical
Pancreatic enzyme maturation occurs over the first 2 to 3 years of life.
Clinical
MR pancreatic function testing (MRPFT) acquires identical fluid-sensitive imaging pre- and post-secretin, then quantifies the volume of fluid secreted into the gastrointestinal tract.
ClinicalAndrew Trout
In the MRPFT protocol, there is about a 15-minute delay between pre- and post-secretin imaging to allow fluid accumulation.
ClinicalAndrew Trout
MRPFT can threshold images and quantify secreted fluid volume by subtracting pre-secretin fluid from post-secretin fluid.
ClinicalAndrew Trout
Correlation between MRPFT volumetric analysis and endoscopic pancreatic function testing is under study in about 35 patients.
ClinicalAndrew Trout
Qualitative assessment of exocrine function by MRPFT may differ between pediatric and adult patients, possibly due to size or weight dependency.
OpinionAndrew Trout
In chronic pancreatitis patients with dilated and abnormal ducts at baseline, secretin may not add diagnostic value for duct visualization, though it is used primarily for exocrine assessment.
OpinionAndrew Trout
Pancreatic enzyme replacement may improve bloating and other GI symptoms in patients with exocrine insufficiency, but does not prevent attacks.
ClinicalJoe Palermo
The multidisciplinary pain team comprises a pain physician (medical/psychosocial assessment, medication, interventional procedures), a psychologist (cognitive behavioral therapy, school reintegration, family intervention), and a nurse.
ClinicalDoctor Goldschneider
Psychology involvement is 100% of the time in the pain clinic, not optional, to address pain coping, functional and emotional impact, and school reintegration.
ClinicalDoctor Goldschneider
Opioids are a tool requiring risk assessment, mitigation, informed consent (mandated by Ohio law for chronic use in minors), controlled substance agreements, prescription history tracking, and use of the lowest effective dose.
ClinicalDoctor Goldschneider
In the case of a 13-year-old with annular pancreas and chronic pancreatitis, multidisciplinary pain management (topiramate for migraines, low-dose methadone for 2 years, psychology, family intervention) resulted in pain resolution, return to school and activities, and indefinite deferral of Whipple surgery.
ClinicalDoctor Goldschneider
Between 7 and 34% of pediatric patients with acute pancreatitis will eventually develop recurrent episodes.
Host summaryJoe Palermo · not cited in answers
Acute recurrent pancreatitis is defined as two distinct episodes of acute pancreatitis with either complete resolution between episodes or complete normalization of enzymes between episodes.
Host summaryJoe Palermo · not cited in answers
Chronic pancreatitis requires a combination of clinical presentation and abnormal imaging findings: ductal irregularities, calcifications, or pancreatic gland atrophy, seen on CT, MRCP, or ERCP.
Host summaryJoe Palermo · not cited in answers
Chronic pancreatitis diagnosis also requires abdominal pain consistent with pancreatic origin or evidence of endocrine or exocrine pancreatic insufficiency.
Host summaryJoe Palermo · not cited in answers
In adults, up to 70% of chronic pancreatitis cases are caused by alcohol.
Host summaryJoe Palermo · not cited in answers
PRSS1 (cationic trypsinogen gene) is a gain-of-function gene causing hereditary pancreatitis, autosomal dominant, with 80% penetrance for acute pancreatitis, 50% for chronic pancreatitis, and more than 40% risk of pancreatic cancer.
Host summary
SPINK1 (trypsin inhibitor gene) is a modifier gene, autosomal recessive, but heterozygous patients can also develop disease.
Host summary
Severe CFTR mutations (e.g., delta 508) cause exocrine pancreatic insufficiency; patients who are pancreatic sufficient with CF mutations are at risk for pancreatitis and chronic pancreatitis.
Host summary
CTRC gene has been shown through functional studies to be linked to development of chronic pancreatitis and acute recurrent pancreatitis.
Host summary
Six additional genes beyond the original four (PRSS1, SPINK1, CFTR, CTRC) are now known to be associated with ARP and CP.
Host summary
PRSS1 penetrance is incomplete: half of patients with the gene develop chronic pancreatitis, not all.
Host summary
Low-fat diet, pancreatic enzyme replacement, antioxidants, and steroids have never been shown to prevent recurrent pancreatitis episodes or pancreatic pain episodes.
Host summaryJoe Palermo · not cited in answers
Cognitive behavioral therapy is the standard, state-of-the-art therapy for pain management.
Host summaryDoctor Goldschneider · not cited in answers