StayCurrentMD · ARMs in Female Patients: Pediatric Colorectal Controversies 2014
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Video55 min·Published Apr 2012Older

ARMs in Female Patients: Pediatric Colorectal Controversies 2014

hosted by Dr. Marc Levitt · StayCurrentMD
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What the experts said36 expert statements
Perineal fistula is diagnosed when the fistula opening is at or anterior to the fourchette, with normal urethra and vagina visible
ClinicalMarc Levitt
Vestibular fistula is diagnosed when the fistula opens posterior to the fourchette within the vestibule
ClinicalMarc Levitt
For perineal fistula mobilization, the goal is to mobilize just enough to reach perineal skin with a little bit of tension
OpinionDon
Complete separation from vagina is preferred because incomplete mobilization may lead to retraction and wound problems
OpinionMarc Levitt
In every redo of a female ARM, areolar tissue is found that had never been dissected by the original surgeon
ClinicalMarc Levitt
Inadequate anterior rectal wall mobilization can lead to perineal body disruption as the anterior wall pulls back
ClinicalMarc Levitt
Many newborn female vestibular fistula redos were done without a colostomy
ClinicalDon
The rectal blood supply is intramural, so injuring the rectal wall hurts its blood supply
ClinicalMarc Levitt
Starting laterally before attempting anterior separation is key to avoiding injury when separating rectum from vagina
ClinicalMarc Levitt
Coming in from lateral to anterior and starting more proximally makes separation easier than starting at the perineum
ClinicalDon
Primary vestibular repair without colostomy can be done in newborn or within 3-4 months depending on child's condition
OpinionMarc Levitt
Waiting until perineal body is healed (day 6-7) before feeding allows intervention if dehiscence is developing
OpinionMarc Levitt
10% dextrose can be used for NPO periods up to 7 days in well-nourished children, avoiding need for hyperalimentation
ClinicalMarc Levitt
Systematic review shows early enteral nutrition appears better than later nutrition in ARM patients, but all studies are retrospective and poor quality
EpidemiologicalMarc Levitt
About 2-5% of vestibular fistulas have a vaginal septum
EpidemiologicalMarc Levitt
The ideal time to remove a vaginal septum is when the rectum is being mobilized and the perineal body is open
OpinionMarc Levitt
Women with longitudinal vaginal septum often learn to work around it for intercourse but have problems with tampon use
ClinicalMarc Levitt
Vaginal septum resection in adolescents is not a difficult operation and can be done with electrocautery
ClinicalMarc Levitt
True vaginal fistula (within introitus) is rare and requires slightly more rectal mobilization than vestibular fistula
ClinicalMarc Levitt
Sigmoid colon can be used as neovagina in vestibular fistula with absent vagina
ClinicalDon
Using rectum as vagina and mobilizing proximal bowel as neo-rectum should only be done if patient unlikely to be continent (spinal anomaly, absent sacrum)
OpinionMarc Levitt
In vestibular fistula with absent vagina, 75% have urologic problems including neurogenic bladder
EpidemiologicalDon
Of patients with vestibular fistula and absent vagina, 50% have CKD stage 3 or greater
EpidemiologicalDon
Rectum separates from urethra more easily than from vagina in absent vagina cases, with thick fibrous tissue rather than adherent common wall
ClinicalMarc Levitt
Neovagina is technically easier in younger children because the pedicle reaches more easily in a shorter pelvis
ClinicalMarc Levitt
There are two types of cloacas: lower ones (common channel ≤3 cm) and complicated ones (>3 cm)
ClinicalMarc Levitt
Hydrocolpos in cloaca may obstruct distal ureters and cause bilateral hydronephrosis
ClinicalMarc Levitt
About 50% of cloacas have a duplicated gynecologic system
EpidemiologicalMarc Levitt
For newborn cloaca with hydrocolpos, open divided colostomy with pigtail catheter decompression of vagina is preferred over formal vaginostomy
OpinionMarc Levitt
Attempting cystoscopy at time of colostomy creation in cloaca makes the colostomy very difficult
ClinicalMarc Levitt
Laparoscopic approach for cloaca colostomy allows visualization of pelvic structures and percutaneous vaginostomy tube placement
ClinicalMarc Levitt
Curled tube is preferred over straight tube for vaginostomy because straight tubes fall out at 2 months when inflammation resolves
ClinicalMarc Levitt
Much of hydrocolpos fluid is urine refluxing up, not just vaginal secretions
ClinicalDon
Intermittent catheterization of cloaca 2-3 times daily can drain urine and avoid need for vaginostomy tube in many cases
ClinicalMarc Levitt
Catheterization teaching should be done under ultrasound guidance because tube can go into right vagina, left vagina, bladder, or rectum
ClinicalMarc Levitt
Once hydrocolpos is drained, the bladder can fill, demonstrating that hydrocolpos compresses ureters and prevents bladder filling
ClinicalMarc Levitt