Clinical Characteristics and Postoperative Functional Outcomes in Children With Mowat-Wilson Syndrome and Hirschsprung's Disease: A Single-center Study
Author / Expert
Tianran Cheng, Zhen Zhang, Ruijie Zhou, Weike Liu, Ping Xiao, Lihua Wu, Ya Ma, Wenquan Niu, Yong Chen, Bo Li, Agostino Pierro, Long Li, Qian Jiang, Qi Li
Topic overview
Mowat-Wilson Syndrome (MWS) is a rare autosomal dominant genetic disorder. Approximately half of individuals with MWS present with Hirschsprung's Disease (HSCR). There is no nested case–control study that correlates with its prognosis. This study aimed to compare the mid-to-short-term postoperative prognosis between children with MWS-associated with HSCR and those with isolated HSCR.
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