SKIP SEGMENT HIRSCHSPRUNG DISEASE: UNICENTRIC EXPERIENCE WITH FOUR CASES AND SYSTEMATIC LITERATURE REVIEW
Topic overview
This article examines skip segment Hirschsprung disease, a rare variant where aganglionic bowel segments are interrupted by normally innervated intestine. The authors present four cases from their institution and conduct a systematic literature review to evaluate diagnostic approaches and surgical management strategies for this challenging condition.
Key takeaways
- Skip segment Hirschsprung disease involves non-contiguous aganglionic bowel segments separated by normally ganglionated intestine.
- This variant is rare with only scattered case reports in literature, making evidence-based management challenging.
- Systematic review of existing cases is essential to guide surgical planning and avoid missed aganglionic segments.
- Intraoperative frozen section biopsies at multiple levels are critical to identify all affected bowel segments.
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How to cite: GlobalCastMD. SKIP SEGMENT HIRSCHSPRUNG DISEASE: UNICENTRIC EXPERIENCE WITH FOUR CASES AND SYSTEMATIC LITERATURE REVIEW. GlobalCastMD Medical Library. 2026-02-22. https://library.globalcastmd.com/article/11550
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