Surgical closure of congenital portosystemic shunts in children A modified classification for transitioning to minimal-invasive repair.
Author / Expert
Julian Kolorz, Kristina Kampmann, Elke Lainka, Martin May, Maren Schulze, Stéphanie Franchi-Abella, Sophie Branchereau, Carsten Müntjes, Jens Theyson, Lars Pape, Michael Berger, Simone Kathemann
Topic overview
Congenital portosystemic shunts (CPSS) are rare malformations of visceral vessels that lead to poor or absent intrahepatic portal flow. Therapeutic options have shifted away from liver transplantation towards either interventional or surgical closure with excellent results. The challenge to reliably predict portal venous pressure response to shunt occlusion, paired with significant interindividual variability of shunt anatomy have hindered the structured transition from open to minimal invasive surgical shunt closure.
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