Cardiac-associated biliary atresia (CABA): a prognostic subgroup
Author / Expert
Arch Dis Child (Aldeiri B, Giamouris V, Pushparajah K, Miller O, Baker A, Davenport M. - curated by SCHCP)
Topic overview
Objectives: To describe the range of concurrent cardiac malformations in biliary atresia (BA) while providing a functional framework of risk.
Methods: Demographic and variables were collected from a prospectively maintained single-centre database. Infants were grouped according to a cardiac functional framework (A=acyanotic, B=cyanotic and C=insignificant shunt). Primary outcome was set as clearance of jaundice (bilirubin ≤20 μmol/L) following Kasai portoenterostomy (KPE). Native liver survival and overall actuarial survival were compared with a date-matched control infant with BA (n=77). P value
Comments