Diffuse Esophageal Leiomyomatosis in Pediatric Patients: A Systematic Review and Quality of Evidence Assessment

Systematic review of 58 pediatric DEL cases shows strong association with Alport syndrome (57.7%) and predominant presentation with dysphagia. Esophagectomy with gastric transposition remains standard treatment with 33% complication rate but low mortality (3.5% disease-specific).