Prevalence of Hirschsprung-associated enterocolitis in patients with Hirschsprung disease

Systematic review of 57 studies analyzing 18,312 Hirschsprung disease patients reveals preoperative enterocolitis prevalence of 18.3% overall, increasing with aganglionic segment length (26.1% in total colonic aganglionosis). Postoperative HAEC risk remains comparable at 18.2% regardless of surgical technique employed.