StayCurrentMD · Physiology: Pectus Innovations
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Video21 min·Published Oct 2015Older

Physiology: Pectus Innovations

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What the experts said42 expert statements · 2 host summaries
Older pectus patients report progressive exercise intolerance and breathing difficulty developing over the last decade after being asymptomatic their whole life.
ClinicalDawn
99% of pectus patients have transthoracic echocardiograms reported as normal with no issues.
ClinicalDawn
Transthoracic echo has difficulty obtaining adequate windows to visualize the right side of the heart in pectus patients.
ClinicalDawn
Intraoperative transesophageal echocardiography shows marked improvement in right ventricular chamber dimensions after pectus repair.
ClinicalDawn
Flow velocity through the right ventricular outflow tract nearly triples after pectus repair.
ClinicalDawn
Left ventricular output significantly improves when right ventricular flow increases after pectus repair because the heart functions as a pump.
ClinicalDawn
Cardiac output can improve from 55% (normal range) to 77% after pectus repair in older patients, with patients noticing improved exercise capacity and reduced fatigue.
ClinicalDawn
Cardiac contractility, synchrony, and mobility show significant differences between pre-operative and post-operative states in pectus patients.
ClinicalDawn
The efficiency of the cardiac pump improves after pectus repair, likely due to correction of heart distortion and right ventricular chamber deflection.
ClinicalDawn
In a series of 168 patients, minimally invasive repair (MIRP) showed 30% increase in cardiac output while open repair showed less improvement, possibly because open cases include mixed pathology like malunion.
ClinicalDawn
Overall cardiac output increased 24% across all pectus repair patients in the series.
ClinicalDawn
Pectus excavatum is a medical disease, not cosmetic, and affects patients physiologically, with worsening tolerance to compression as they age.
OpinionDawn
Standard Bruce protocol ischemic stress testing is not appropriate for pectus evaluation unless ischemia is suspected; cardiopulmonary exercise testing is needed instead.
ClinicalDawn
Cardiopulmonary exercise testing evaluates VO2 max and anaerobic VO2, which are very abnormal in pectus patients while other parameters remain normal, and separates cardiac from pulmonary components.
ClinicalDawn
A French study of 125 adults showed cardiopulmonary exercise parameters statistically improve and normalize after surgical pectus repair.
EpidemiologicalDawn
Pectus patients show limited ability to increase stroke volume during exercise; output initially increases by heart rate but plateaus when volume increase is needed due to chest cage restriction, appearing as a flat line rather than the normal upward slope.
ClinicalDawn
The flat stroke volume response to exercise improves statistically significantly after pectus repair.
ClinicalDawn
Cardiopulmonary exercise testing is used routinely in congenital heart disease to assess functional capacity and guide decisions about palliation and conduit replacement.
ClinicalMichael
Cardiopulmonary exercise testing has not been performed frequently for pectus patients because surgical decisions have been made on other bases and testing has not been required.
ClinicalMichael
Cardiopulmonary exercise testing would be a good tool for borderline pectus cases where there is uncertainty about proceeding with surgery.
OpinionMichael
Ehlers-Danlos type 4 (vascular type) does not typically present with pectus excavatum as it is not primarily a skeletal or hypermobile disorder.
Clinical
Ehlers-Danlos type 4 involves internal tissue fragility requiring specially managed repairs, and would require careful consideration before proceeding with pectus surgery.
Clinical
Genetic testing should be performed to confirm Ehlers-Danlos type 4, and skin biopsy may be needed if genetic testing is normal but clinical suspicion remains high.
Clinical
Patients frequently self-diagnose Ehlers-Danlos vascular type based on internet research, visible veins, or family history of abdominal aortic aneurysm, none of which actually indicate the disorder.
Clinical
There is no genetic disorder that represents an absolute contraindication to pectus surgery, only relative contraindications based on functional status.
Opinion
Very young children may outgrow their pectus bars and require explantation and replacement, representing a cost of early repair.
ClinicalDawn
Adolescents who are nearly completely grown may have better cost-benefit ratio for pectus repair compared to very young children.
OpinionDawn
A seven-year-old with severe symptomatic pectus may need earlier repair despite general preference to wait.
OpinionDawn
An Easter Seals grant study at UCLA using cardiopulmonary exercise testing in children showed that while some classes of patients had deficits, a large percentage of children did not show problems.
EpidemiologicalDawn
Compensation mechanisms work better in younger pectus patients; deficits become more apparent on testing as patients age.
ClinicalDawn
Some children are completely asymptomatic and progress to become symptomatic as they age, while others are symptomatic when very young.
ClinicalDawn
Young children have more pliable chest walls, allowing repair with minimal force (described as 'a popsicle stick'), while adults have tremendous pain due to chest wall rigidity.
ClinicalDawn
In Korea, pectus repairs are performed on 3-4-5 year olds using very small bar sets.
ClinicalDawn
The trend in the United States has shifted from repairing pectus patients young to repairing them at older ages.
EpidemiologicalDawn
The institution where Donald Nuss practices has moved away from performing pectus repairs on young children, suggesting they encountered more issues than reported in initial series, possibly identified during long-term follow-up.
ClinicalDawn
Korean surgeons (specifically Yung Park) routinely repair pectus in young children and report no problems, considering it unusual to wait until older ages.
ClinicalDawn
Vacuum bell therapy works if the patient has a very flexible chest and wears the device religiously.
ClinicalDawn
Patient compliance with vacuum bell therapy varies greatly, with many young children tolerating it for only short periods despite parental efforts.
ClinicalDawn
Vacuum bell therapy is recommended for very young children (e.g., 5 years old) as an alternative to operative repair.
OpinionDawn
Dawn has selection bias in her practice because she predominantly sees symptomatic pectus patients, while thousands of asymptomatic adults with pectus likely exist.
OpinionDawn
95% of patients presenting to Dawn's office are seeking surgery.
EpidemiologicalDawn
When discussing testing results with pectus patients, they often reveal subtle symptoms they had not previously recognized or reported, such as reduced exercise capacity compared to peers.
ClinicalDawn
Pectus operations are better tolerated when patients are younger, but older patients require substantial narcotics for pain control.
Host summary
Donald Nuss initially performed pectus repairs on very young patients, as young as 3 years of age, without high recurrence rates in his early series.
Host summary