New article you should know about From JPS by Dr. Cecilia GIgena
"Pectus Arcuatum: A Pectus Unlike Any Other"
Authors: Sarah Abdellaoui, Aurélien Scalabre, Christian Piolat, Frédéric Lavrand, Amane-Allah Lachkar, Anne Lehn, Clémence Klipfel, Brice Henry, Valentin Soldea, Frédéric Hameury, François Becmeur
Full article: https://gcmd.co/48bwRZ9
Background
Pectus arcuatum is often mistaken for a type of pectus carinatum. However, pectus arcuatum is a unique clinical form of pectus caused by premature obliteration of the sternal sutures (manubrial sternum, four sternebrae and xiphoïd process), whereas pectus carinatum is due to abnormal growth of the costal cartilage. In order to better describe pectus arcuatum, we analysed the files of patients with pectus arcuatum followed in our centers.
Methods
Multicenter retrospective study of young patients’ files diagnosed with pectus arcuatum.
Results
The clinical diagnosis of pectus arcuatum was made in 34 patients with a mean age at diagnosis of 10.3 years (4–23 years). A chest profile X-ray or a CT scan was performed in 16 patients (47%) and confirmed the diagnosis of PA by the presence of a sternal fusion. It was complete in 12 patients. A malformation was associated in 35% of cases (Noonan syndrome 33%, scoliosis 25% or cardiopathy 16%). 11 patients (32%) had a family history of skeletal malformation. Orthopedic treatment was initiated in 3 patients without any success. 11 patients underwent surgical correction, which was completed in 7 of them.
Conclusion
The diagnosis of pectus arcuatum is based on clinical experience and if necessary, on a profile chest X-ray showing the fusion of the sternal pieces. It implies the search for any associated malformations (musculoskeletal, cardiac, syndromic). Bracing treatment is useless for pectus arcuatum. Corrective surgery, based on a sternotomy associated with a partial chondro-costal resection, can be performed at the end of growth.
Type: video · 0 min · posted 2024-01-17 Canonical: https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899 ## Chapters - [0:00](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=0) Pectus Arcuatum: Diagnosis and Management ## Statements - "The study is a multi-center retrospective study conducted in France describing pectus arcuatum" — Cecilia Gigena (epidemiological) [0:11](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=11) - "The study included 34 patients with pectus arcuatum" — Cecilia Gigena (epidemiological) [0:20](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=20) - "47% of patients needed chest x-ray or CT scan to confirm the diagnosis of pectus arcuatum" — Cecilia Gigena (clinical) [0:20](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=20) - "35% of pectus arcuatum patients were associated with a malformation" — Cecilia Gigena (epidemiological) [0:29](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=29) - "Noonan syndrome is an associated malformation seen with pectus arcuatum" — Cecilia Gigena (clinical) [0:29](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=29) - "Scoliosis is an associated malformation seen with pectus arcuatum" — Cecilia Gigena (clinical) [0:29](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=29) - "The best treatment for pectus arcuatum was surgical correction that included a sternotomy" — Cecilia Gigena (clinical) [0:29](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=29) - "Pectus arcuatum should not be confused with pectus carinatum as they are different conditions" — Cecilia Gigena (clinical) [0:41](https://library.globalcastmd.com/watch/pectus-arcuatum-a-pectus-unlike-any-other-7899?t=41) ## Transcript Have you ever treated a pectussarquatum like a pectus carinatum? Hi, I'm Cecilia Gena from Cincinnati Children's Hospital, and I think this is an article that you should know about. This is a multi-center retrospective study done in France, and they wanted to better describe the pectussarquantum. And what did they find? They have 34 patients, 47% needed a chest x-ray or a CT scan to confirm the diagnosis. 35% of the patients were associated with a malformation, like Noonan's syndrome or scoliosis, and the best treatment was a surgical correction that included an astronomy. So be aware of this difference. Do not confusefectus or quatum with thefectus carinatum. Let us know what you think and stay tuned for more articles that you should know about. --- Not medical advice · citation policy: https://library.globalcastmd.com/ai