Cardiac-associated biliary atresia (CABA): a prognostic subgroup
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Read the article on pubmed.ncbi.nlm.nih.gov ↗Article · Sep 2020 · 1 min read
In brief
In brief
Study examining outcomes in biliary atresia patients with concurrent cardiac malformations, categorized by cardiac functional severity. Findings show cardiac-associated BA represents a distinct prognostic subgroup with implications for surgical timing and native liver survival following Kasai portoenterostomy.
Written by the GCMD Library team from the article.
Objectives: To describe the range of concurrent cardiac malformations in biliary atresia (BA) while providing a functional framework of risk.
Methods: Demographic and variables were collected from a prospectively maintained single-centre database. Infants were grouped according to a cardiac functional framework (A=acyanotic, B=cyanotic and C=insignificant shunt). Primary outcome was set as clearance of jaundice (bilirubin ≤20 μmol/L) following Kasai portoenterostomy (KPE). Native liver survival and overall actuarial survival were compared with a date-matched control infant with BA (n=77). P value